Introduction: Osteogenesis Imperfecta is a rare condition that can be very disabling. It is an inherited disease of the bones, which is characterized by fragility that causes affected individuals to have recurrent fractures that subsequently lead to pain, deformity and disability. The aim of the study was to determine the prevalence of Osteogenesis Imperfecta and identify the common deformities and treatment methods used in managing affected individuals at the Zambia Italian Orthopedics Hospital. Methods: This was a retrospective cross sectional survey. A data capture sheet was used to collect data from records and descriptive trend analysis was done in excel. Results: We identified 18 patients with Osteogenesis Imperfecta out of 8250. The age range was 1 to 17 years. Eighty-three percent (n=15) of these patients had deformities which included; bowed lower limbs, scoliosis and other related complications. All the patients underwent surgery at one point in time and received physiotherapy. Conclusion: The prevalence of Osteogenesis Imperfecta at the Zambia Italian Orthopaedics Hospital Community Based Rehabilitation Project is low. Surgery is the most commonly used method of treatment coupled with physiotherapy. Though uncommon, the condition is expensive to manage for both the institution and affected individuals’ families. This is as a result of repeated surgeries and prolonged physiotherapy.
| Published in | Science Journal of Public Health (Volume 3, Issue 5) |
| DOI | 10.11648/j.sjph.20150305.40 |
| Page(s) | 804-807 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2015. Published by Science Publishing Group |
Osteogenesis Imperfecta, Surgery, Physiotherapy, Orthopedics, Disability, Rehabilitation
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APA Style
Stella Kabengo, Esther Munalula-Nkandu, James C. Munthali, Loveness A. Nkhata, Hastings Shula. (2015). The Prevalence and Characteristics of Patients Diagnosed with Osteogenesis Imperfecta at the Zambia Italian Orthopedics Hospital Community Based Rehabilitation Project. Science Journal of Public Health, 3(5), 804-807. https://doi.org/10.11648/j.sjph.20150305.40
ACS Style
Stella Kabengo; Esther Munalula-Nkandu; James C. Munthali; Loveness A. Nkhata; Hastings Shula. The Prevalence and Characteristics of Patients Diagnosed with Osteogenesis Imperfecta at the Zambia Italian Orthopedics Hospital Community Based Rehabilitation Project. Sci. J. Public Health 2015, 3(5), 804-807. doi: 10.11648/j.sjph.20150305.40
AMA Style
Stella Kabengo, Esther Munalula-Nkandu, James C. Munthali, Loveness A. Nkhata, Hastings Shula. The Prevalence and Characteristics of Patients Diagnosed with Osteogenesis Imperfecta at the Zambia Italian Orthopedics Hospital Community Based Rehabilitation Project. Sci J Public Health. 2015;3(5):804-807. doi: 10.11648/j.sjph.20150305.40
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Download@article{10.11648/j.sjph.20150305.40,
author = {Stella Kabengo and Esther Munalula-Nkandu and James C. Munthali and Loveness A. Nkhata and Hastings Shula},
title = {The Prevalence and Characteristics of Patients Diagnosed with Osteogenesis Imperfecta at the Zambia Italian Orthopedics Hospital Community Based Rehabilitation Project},
journal = {Science Journal of Public Health},
volume = {3},
number = {5},
pages = {804-807},
doi = {10.11648/j.sjph.20150305.40},
url = {https://doi.org/10.11648/j.sjph.20150305.40},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.sjph.20150305.40},
abstract = {Introduction: Osteogenesis Imperfecta is a rare condition that can be very disabling. It is an inherited disease of the bones, which is characterized by fragility that causes affected individuals to have recurrent fractures that subsequently lead to pain, deformity and disability. The aim of the study was to determine the prevalence of Osteogenesis Imperfecta and identify the common deformities and treatment methods used in managing affected individuals at the Zambia Italian Orthopedics Hospital. Methods: This was a retrospective cross sectional survey. A data capture sheet was used to collect data from records and descriptive trend analysis was done in excel. Results: We identified 18 patients with Osteogenesis Imperfecta out of 8250. The age range was 1 to 17 years. Eighty-three percent (n=15) of these patients had deformities which included; bowed lower limbs, scoliosis and other related complications. All the patients underwent surgery at one point in time and received physiotherapy. Conclusion: The prevalence of Osteogenesis Imperfecta at the Zambia Italian Orthopaedics Hospital Community Based Rehabilitation Project is low. Surgery is the most commonly used method of treatment coupled with physiotherapy. Though uncommon, the condition is expensive to manage for both the institution and affected individuals’ families. This is as a result of repeated surgeries and prolonged physiotherapy.},
year = {2015}
}
TY - JOUR T1 - The Prevalence and Characteristics of Patients Diagnosed with Osteogenesis Imperfecta at the Zambia Italian Orthopedics Hospital Community Based Rehabilitation Project AU - Stella Kabengo AU - Esther Munalula-Nkandu AU - James C. Munthali AU - Loveness A. Nkhata AU - Hastings Shula Y1 - 2015/10/19 PY - 2015 N1 - https://doi.org/10.11648/j.sjph.20150305.40 DO - 10.11648/j.sjph.20150305.40 T2 - Science Journal of Public Health JF - Science Journal of Public Health JO - Science Journal of Public Health SP - 804 EP - 807 PB - Science Publishing Group SN - 2328-7950 UR - https://doi.org/10.11648/j.sjph.20150305.40 AB - Introduction: Osteogenesis Imperfecta is a rare condition that can be very disabling. It is an inherited disease of the bones, which is characterized by fragility that causes affected individuals to have recurrent fractures that subsequently lead to pain, deformity and disability. The aim of the study was to determine the prevalence of Osteogenesis Imperfecta and identify the common deformities and treatment methods used in managing affected individuals at the Zambia Italian Orthopedics Hospital. Methods: This was a retrospective cross sectional survey. A data capture sheet was used to collect data from records and descriptive trend analysis was done in excel. Results: We identified 18 patients with Osteogenesis Imperfecta out of 8250. The age range was 1 to 17 years. Eighty-three percent (n=15) of these patients had deformities which included; bowed lower limbs, scoliosis and other related complications. All the patients underwent surgery at one point in time and received physiotherapy. Conclusion: The prevalence of Osteogenesis Imperfecta at the Zambia Italian Orthopaedics Hospital Community Based Rehabilitation Project is low. Surgery is the most commonly used method of treatment coupled with physiotherapy. Though uncommon, the condition is expensive to manage for both the institution and affected individuals’ families. This is as a result of repeated surgeries and prolonged physiotherapy. VL - 3 IS - 5 ER -
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